Rare Case of Metastatic Pleomorphic Liposarcoma of Thigh Presenting as Ewing’s Sarcoma

  • Sandip Giri Fellow Oncoimaging and intervention,Department of Radiodiagnosis, Tata Medical Center, India
  • Anisha Gehani Department of Radiodiagnosis, Tata Medical Center, India
  • Sheena Alphones Department of Pathology,Tata Medical Center, India
  • Divya Midha Department of Pathology,Tata Medical Center, India
  • Dibash Baral Nepal Health Research Council, ramshah path Kathmandu, Nepal

Abstract

Liposarcoma is an uncommon group of tumors in the pediatric population. Of the various known subtypes,pleomorphic liposarcoma is the most infrequent in children.We present the case of a 7-year old child coming to the radiology department for evaluation of a right knee swelling. Plain radiograph and corresponding MRI images showed features of primary bone tumor possibly Ewing’s sarcoma in right distal femur. The child developed right shoulder pain and CT thorax abdomen was done which revealed retroperitoneal mass with hepatic and pulmonary metastases.Subsequent core needle biopsy from the femur confirmed metastatic liposarcoma with pleomorphic features, extremely rare in childhood.The very rare incidence of metastasis that too presenting as a common primary tumor the misdiagnosis of which could result in catastrophic fate. So it’s of prime importance that clinicians should be aware of this entity.
Keywords: FISH; liposarcoma; myxiod dedifferentiated liposarcoma; pleomorphic liposarcoma; softsarcoma

Published
2021-04-23
How to Cite
Giri , S., Gehani, A., Alphones , S., Midha, D., & Baral, D. (2021). Rare Case of Metastatic Pleomorphic Liposarcoma of Thigh Presenting as Ewing’s Sarcoma. Journal of Nepal Health Research Council, 19(1), 215-217. https://doi.org/10.33314/jnhrc.v19i1.3324